Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001571667 | SCV001796179 | uncertain significance | not provided | 2019-12-16 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; Not observed in large population cohorts (Lek et al., 2016); Frameshift variant predicted to result in protein truncation as the last 43 amino acids are lost and replaced with 8 incorrect amino acids, although loss-of-function variants have not been reported downstream of this position in the protein; Occurs in an alternate transcript where no variants have been reported in the Human Gene Mutation Database in association with EYA4-related disorders (Stenson et al., 2014) |
Laboratory of Prof. |
RCV004584919 | SCV005073747 | pathogenic | Autosomal dominant nonsyndromic hearing loss 10 | 2024-05-08 | criteria provided, single submitter | research | A frameshit variant in a known dominant deafness gene in which allframeshifts known variants are pathogenic |