Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000223505 | SCV000271222 | likely pathogenic | Rare genetic deafness | 2015-05-21 | criteria provided, single submitter | clinical testing | The c.371-2A>C variant in EYA4 has not been previously reported in individuals w ith hearing loss or in large population studies. This variant occurs in the inva riant region (+/- 1,2) of the splice consensus sequence and is predicted to caus e altered splicing leading to an abnormal or absent protein. In summary, althoug h additional studies are required to fully establish its clinical significance, the c.371-2A>C variant is likely pathogenic. |