Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004727086 | SCV005333170 | pathogenic | not provided | 2023-09-20 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect on long-term inactivation of voltage-gated sodium channels (Fry et al., 2021); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 33245860) |
OMIM | RCV001292556 | SCV001481128 | pathogenic | Developmental and epileptic encephalopathy, 90 | 2021-02-19 | no assertion criteria provided | literature only |