Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000818060 | SCV000958655 | pathogenic | Mitochondrial complex II deficiency, nuclear type 1; Paragangliomas 5 | 2018-08-08 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Ser208Leufs*18) in the SDHA gene. It is expected to result in an absent or disrupted protein product. This variant is not present in population databases (ExAC no frequency). For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in SDHA are known to be pathogenic (PMID: 22974104, 24781757). This variant has not been reported in the literature in individuals with SDHA-related disease. |