Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003337759 | SCV004048020 | uncertain significance | Developmental and epileptic encephalopathy, 41 | criteria provided, single submitter | clinical testing | The missense variant c.1003A>G (p.Ile335Val) in SLC1A2 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Ile335Val variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. The amino acid Ile at position 335 is changed to a Val changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Ile335Val in SLC1A2 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Variant of Uncertain Significance (VUS). |