Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neurogenetics, |
RCV003231068 | SCV003928205 | uncertain significance | Developmental and epileptic encephalopathy, 41 | 2023-06-02 | criteria provided, single submitter | clinical testing | The Ala432Asp variant was identified in a patient who was later diagnosed with Angelman syndrome. Confirmation of Angelman syndrome was achieved through methylation analysis and CNV analysis, which revealed a deletion at position hg19 chr15:23684685_28197044. Unfortunately, segregation analysis could not be performed due to the unavailability of family samples. It is noteworthy that the clinical presentation of the proband was more severe compared to typical patients with Angelman syndrome. |