Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Undiagnosed Diseases Network, |
RCV000735220 | SCV000863428 | uncertain significance | AIFM1-related hypomyelination with spondylometaphyseal dysplasia | 2018-09-06 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV000856717 | SCV001521363 | pathogenic | Spondyloepimetaphyseal dysplasia, Bieganski type | 2020-06-01 | criteria provided, single submitter | clinical testing | This variant was determined to be pathogenic according to ACMG Guidelines, 2015 [PMID:25741868]. |
Ambry Genetics | RCV002370001 | SCV002673864 | likely benign | Inborn genetic diseases | 2019-07-11 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
OMIM | RCV000856717 | SCV000999261 | pathogenic | Spondyloepimetaphyseal dysplasia, Bieganski type | 2019-11-27 | no assertion criteria provided | literature only |