Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Medical Genetics and Applied Genomics, |
RCV003486006 | SCV004232728 | pathogenic | Mandibulofacial dysostosis-microcephaly syndrome | 2024-01-29 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004723336 | SCV005331599 | pathogenic | not provided | 2024-01-16 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; This variant is associated with the following publications: (PMID: 35395430) |
Clinical Genetics Laboratory, |
RCV005242402 | SCV005889716 | pathogenic | Mandibulofacial dysostosis | 2024-12-27 | criteria provided, single submitter | clinical testing | Observed in a heterozygous state (de novo) at our lab in a patient with matching phenotype. ACMG criteria used: PVS1, PS2, PS4, PM2 |