Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000532921 | SCV000648615 | likely benign | Neuroblastoma, susceptibility to, 3 | 2024-01-18 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004719868 | SCV005325509 | uncertain significance | not provided | 2023-09-25 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Observed in a pediatric T-cell acute lymphoblastic leukemia patient (PMID: 31721781); This variant is associated with the following publications: (PMID: 31721781) |
Ambry Genetics | RCV004948439 | SCV005596502 | benign | Hereditary cancer-predisposing syndrome | 2024-08-20 | criteria provided, single submitter | clinical testing | This alteration is classified as benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Prevention |
RCV003900208 | SCV004717681 | likely benign | ALK-related disorder | 2020-12-24 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |