Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000163765 | SCV000214346 | pathogenic | Hereditary cancer-predisposing syndrome | 2017-05-08 | criteria provided, single submitter | clinical testing | The c.216dupT pathogenic mutation, located in coding exon 2 of the BMPR1A gene, results from a duplication of T at nucleotide position 216, causing a translational frameshift with a predicted alternate stop codon (p.N73*). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |
Myriad Genetics, |
RCV003335153 | SCV004044418 | pathogenic | Juvenile polyposis syndrome | 2023-05-25 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a termination codon and is predicted to result in premature protein truncation. |