Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002426220 | SCV002743025 | pathogenic | Hereditary cancer-predisposing syndrome | 2015-12-10 | criteria provided, single submitter | clinical testing | The p.R9* pathogenic mutation (also known as c.25A>T), located in coding exon 1 of the BMPR1A gene, results from an A to T substitution at nucleotide position 25. This changes the amino acid from an arginine to a stop codon within coding exon 1. Since premature stop codons are typically deleterious in nature, this alteration is interpreted as a disease-causing mutation (ACMG Recommendations for Standards for Interpretation and Reporting of Sequence Variations. Revision 2007. Genet Med. 2008;10:294). |
Myriad Genetics, |
RCV003336741 | SCV004043681 | pathogenic | Juvenile polyposis syndrome | 2023-05-25 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a termination codon and is predicted to result in premature protein truncation. |
Baylor Genetics | RCV003475386 | SCV004212658 | likely pathogenic | Polyposis syndrome, hereditary mixed, 2 | 2023-04-27 | criteria provided, single submitter | clinical testing |