Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
All of Us Research Program, |
RCV004012465 | SCV004842992 | uncertain significance | Juvenile polyposis syndrome | 2023-11-30 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004950777 | SCV005539116 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-10-05 | criteria provided, single submitter | clinical testing | The p.I296F variant (also known as c.886A>T), located in coding exon 8 of the BMPR1A gene, results from an A to T substitution at nucleotide position 886. The isoleucine at codon 296 is replaced by phenylalanine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |