Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000552405 | SCV000637709 | uncertain significance | Hereditary diffuse gastric adenocarcinoma | 2023-10-22 | criteria provided, single submitter | clinical testing | This sequence change replaces valine, which is neutral and non-polar, with leucine, which is neutral and non-polar, at codon 425 of the CDH1 protein (p.Val425Leu). This variant is present in population databases (rs570930882, gnomAD 0.01%). This variant has not been reported in the literature in individuals affected with CDH1-related conditions. ClinVar contains an entry for this variant (Variation ID: 463706). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV000583760 | SCV000689441 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-04-09 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV004568801 | SCV005060100 | uncertain significance | Familial cancer of breast | 2024-01-16 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000583760 | SCV005095383 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-06-17 | criteria provided, single submitter | clinical testing | The p.V425L variant (also known as c.1273G>C), located in coding exon 9 of the CDH1 gene, results from a G to C substitution at nucleotide position 1273. The valine at codon 425 is replaced by leucine, an amino acid with highly similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |