Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000639223 | SCV000760793 | uncertain significance | Hereditary diffuse gastric adenocarcinoma | 2023-03-04 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with CDH1-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant  is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 532450). This variant is present in population databases (no rsID available, gnomAD 0.008%). This sequence change replaces glutamine, which is neutral and polar, with glutamic acid, which is acidic and polar, at codon 448 of the CDH1 protein (p.Gln448Glu). |
Ambry Genetics | RCV001010966 | SCV001171236 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-12-24 | criteria provided, single submitter | clinical testing | The p.Q448E variant (also known as c.1342C>G), located in coding exon 10 of the CDH1 gene, results from a C to G substitution at nucleotide position 1342. The glutamine at codon 448 is replaced by glutamic acid, an amino acid with highly similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Gene |
RCV003235321 | SCV003933093 | uncertain significance | not provided | 2022-12-13 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 15235021, 22850631) |
Baylor Genetics | RCV004568407 | SCV005060142 | uncertain significance | Familial cancer of breast | 2023-11-16 | criteria provided, single submitter | clinical testing |