Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV000774142 | SCV000907843 | pathogenic | Hereditary cancer-predisposing syndrome | 2020-07-13 | criteria provided, single submitter | clinical testing | This variant deletes 2 nucleotides in exon 10 of the CDH1 gene, creating a frameshift and premature translation stop signal. This variant is expected to result in an absent or non-functional protein product. This variant has been reported in individuals affected with diffuse gastric cancer and breast cancer (PMID: 17221870, 17545690, 21271559). This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). Loss of CDH1 function is a known mechanism of disease (clinicalgenome.org). Based on the available evidence, this variant is classified as Pathogenic. |
Ambry Genetics | RCV000774142 | SCV002697675 | pathogenic | Hereditary cancer-predisposing syndrome | 2022-07-07 | criteria provided, single submitter | clinical testing | The c.1397_1398delTC variant, located in coding exon 10 of the CDH1 gene, results from a deletion of two nucleotides at nucleotide positions 1397 to 1398, causing a translational frameshift with a predicted alternate stop codon (p.L466Hfs*16). This alteration has been observed in at least two families with a history of gastric cancer (at least one confirmed diffuse gastric cancer in each family) and breast cancer (Kaurah P et al. JAMA, 2007 Jun;297:2360-72; More H et al. Hum Mutat, 2007 Feb;28:203). This variant is considered to be rare based on population cohorts in the Genome Aggregation Database (gnomAD). Of note, this alteration is also designated as c.1391_1392delTC (p.Leu472HisfsX481) in published literature. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |
Myriad Genetics, |
RCV003336179 | SCV004044374 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2023-06-13 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a frameshift predicted to result in premature protein truncation. |