Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001189119 | SCV001356324 | pathogenic | Hereditary cancer-predisposing syndrome | 2020-09-20 | criteria provided, single submitter | clinical testing | This variant deletes 1 nucleotide in exon 11 of the CDH1 gene, creating a premature translation stop signal. This variant is expected to result in an absent or non-functional protein product. To our knowledge, functional studies have not been reported for this variant. This variant has been reported in two related individuals affected with diffuse gastric cancer (PMID: 11968084). This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). Loss of CDH1 function is a known mechanism of disease (clinicalgenome.org). Based on the available evidence, this variant is classified as Pathogenic. |
Labcorp Genetics |
RCV001384476 | SCV001583981 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2021-12-24 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 926514). This premature translational stop signal has been observed in individual(s) with diffuse gastric cancer (PMID: 11968084). This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Asn570Lysfs*14) in the CDH1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CDH1 are known to be pathogenic (PMID: 15235021, 20373070). |
Myriad Genetics, |
RCV001384476 | SCV004045263 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2023-06-14 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a frameshift predicted to result in premature protein truncation. |