Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000129247 | SCV000184006 | likely benign | Hereditary cancer-predisposing syndrome | 2018-08-09 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000034707 | SCV000888029 | benign | not provided | 2018-01-03 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000129247 | SCV002529104 | likely benign | Hereditary cancer-predisposing syndrome | 2021-10-07 | criteria provided, single submitter | curation | |
Biesecker Lab/Clinical Genomics Section, |
RCV000034707 | SCV000043248 | variant of unknown significance | not provided | 2012-07-13 | no assertion criteria provided | research | Converted during submission to Uncertain significance. |
Prevention |
RCV003924898 | SCV004738654 | uncertain significance | CDH1-related disorder | 2023-12-29 | no assertion criteria provided | clinical testing | The CDH1 c.2077G>A variant is predicted to result in the amino acid substitution p.Gly693Ser. This variant has been reported in an individual from an exome sequencing cohort (Johnson et al. 2012. PubMed ID: 22703879). It is reported in 0.0077% of alleles in individuals of European (Non-Finnish) descent in gnomAD and has interpretations in ClinVar of benign and likely benign (https://www.ncbi.nlm.nih.gov/clinvar/variation/41785/). Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |