Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003511713 | SCV004312481 | uncertain significance | Hereditary diffuse gastric adenocarcinoma | 2023-08-06 | criteria provided, single submitter | clinical testing | Studies have shown that this missense change alters CDH1 gene expression (PMID: 35327954). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. This missense change has been observed in individuals with diffuse gastric cancer (PMID: 35327954; Invitae). This variant is not present in population databases (gnomAD no frequency). This sequence change replaces glycine, which is neutral and non-polar, with arginine, which is basic and polar, at codon 761 of the CDH1 protein (p.Gly761Arg). |