Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000215264 | SCV000275625 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-03-08 | criteria provided, single submitter | clinical testing | The p.D764E variant (also known as c.2292C>A), located in coding exon 14 of the CDH1 gene, results from a C to A substitution at nucleotide position 2292. The aspartic acid at codon 764 is replaced by glutamic acid, an amino acid with highly similar properties. This variant was reported in at least one individual with features consistent with CDH1-related diffuse gastric and lobular breast cancer (DGLBC) (Garcia-Pelaez J et al. Lancet Oncol, 2023 Jan;24:91-106; Lee CYC et al. Lancet Oncol, 2023 Jan;24:107-116). This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV001066681 | SCV001231697 | uncertain significance | Hereditary diffuse gastric adenocarcinoma | 2023-09-03 | criteria provided, single submitter | clinical testing | This sequence change replaces aspartic acid, which is acidic and polar, with glutamic acid, which is acidic and polar, at codon 764 of the CDH1 protein (p.Asp764Glu). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with CDH1-related conditions. ClinVar contains an entry for this variant (Variation ID: 231701). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV000215264 | SCV001356363 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-06-20 | criteria provided, single submitter | clinical testing | |
European Reference Network on Genetic Tumour Risk Syndromes |
RCV001066681 | SCV003926914 | uncertain significance | Hereditary diffuse gastric adenocarcinoma | 2022-08-01 | criteria provided, single submitter | clinical testing | PM2 (PMID: 30311375) |
Baylor Genetics | RCV003462474 | SCV004215680 | uncertain significance | Familial cancer of breast | 2023-08-04 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004721307 | SCV005327343 | uncertain significance | not provided | 2023-11-27 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Observed in two individuals from one family meeting testing criteria for HDGC and considered a Variant of Unknown Significance by the authors (PMID: 36509094); This variant is associated with the following publications: (PMID: 36436516, 28688938, 15235021, 22850631, 36509094) |