Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV003328338 | SCV001142213 | likely benign | CDH1-related diffuse gastric and lobular breast cancer syndrome | 2023-08-17 | reviewed by expert panel | curation | The c.49-8C>T is an intronic variant in the splice acceptor region of intron 1. This variant has an allele frequency of 0.00001 (2/150178) in gnomAD with a maximum frequency of 0.00003 (2/57282) in the European (Non-Finnish) sub-population. This variant has been reported in at least 12 individuals without DGC, SRC tumours or LBC and whose families do not suggest HDGC (BS2; SCV000529519.4, SCV000557406.3). This variant is predicted to have no impact on splicing by multiple in silico splice site predictors. HumanSpliceFinder predicts that this variant may create an exonic ESS site, but this effect has not been demonstrated experimentally to our knowledge (BP4). In summary, this variant meets criteria to be classified as likely benign based on ACMG/AMP criteria applied as specified by the CDH1 Variant Curation Expert Panel (Variant Interpretation Guidelines Version 3.1): BS2, BP4. |
Gene |
RCV001712389 | SCV000529519 | likely benign | not provided | 2020-06-03 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000991077 | SCV000557406 | likely benign | Hereditary diffuse gastric adenocarcinoma | 2024-01-11 | criteria provided, single submitter | clinical testing | |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000422103 | SCV000600991 | uncertain significance | not specified | 2016-11-28 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000776443 | SCV000911955 | likely benign | Hereditary cancer-predisposing syndrome | 2018-03-20 | criteria provided, single submitter | clinical testing | |
Myriad Genetics, |
RCV000991077 | SCV005405386 | likely benign | Hereditary diffuse gastric adenocarcinoma | 2024-09-11 | criteria provided, single submitter | clinical testing | This variant is considered likely benign. This variant is intronic and is not expected to impact mRNA splicing. |