Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003145137 | SCV003833315 | uncertain significance | not provided | 2019-07-11 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV003340663 | SCV004047632 | uncertain significance | Bethlem myopathy 2 | criteria provided, single submitter | clinical testing | The c.2594C>G (p.Thr865Arg) missense variant in COL12A1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Thr865Arg variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. The amino acid Thr at position 865 is changed to a Arg changing protein sequence and it might alter its composition and physico-chemical properties. This variant has not been reported to the ClinVar database. The amino acid change p.Thr865Arg in COL12A1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Variant of Uncertain Significance (VUS). |