Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics and Molecular Pathology, |
RCV002466801 | SCV002761476 | uncertain significance | Rubinstein-Taybi syndrome due to CREBBP mutations | 2020-10-18 | criteria provided, single submitter | clinical testing | The CREBBP c.1776G>C variant is classified as VUS (PM2, PP2, PP3) The CREBBP c.1776G>C variant is a single nucleotide change in exon 8 of 31 of the CREBBP gene, which is predicted to change the amino acid tryptophan at position 592 in the protein to cysteine. This variant is absent from population databases (PM2). Absent in gnomAD This is a missense variant in a constrained gene where missense variants are a common mechanism of disease and benign variation is rare (PP2). Computational predictions support a deleterious effect on the gene or gene product (PP3). |