Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002453935 | SCV002616346 | pathogenic | Inborn genetic diseases | 2017-02-28 | criteria provided, single submitter | clinical testing | The p.Q1209* pathogenic mutation (also known as c.3625C>T), located in coding exon 19 of the CREBBP gene, results from a C to T substitution at nucleotide position 3625. This changes the amino acid from a glutamine to a stop codon within coding exon 19. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |
Wessex Regional Genetics Laboratory, |
RCV000856907 | SCV000999440 | pathogenic | Rubinstein-Taybi syndrome due to CREBBP mutations | 2019-11-05 | no assertion criteria provided | clinical testing |