Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics Department, |
RCV003326289 | SCV004032428 | likely benign | Rubinstein-Taybi syndrome due to CREBBP mutations | 2023-01-19 | criteria provided, single submitter | clinical testing | A previously undescribed heterozygous nucleotide sequence variant in the CREBBP gene (16-3739650-T-C) resulting in an amino acid substitution at position 1403 of the protein (p.Asp1403Gly, NM_004380) has been identified. Heterozygous missense variants have been described in patients with OMIM: 180849, Rubinstein-Taybi syndrome 1 and OMIM: 618332, Menke-Hennekam syndrome 1. This variant is not registered in gnomAD. Computational tools classify the variant as pathogenic (PolyPhen-2: 0.997, Sift: 0.0, CADD: 30). According to Sanger sequencing data, the variant is inherited from a healthy father. Based on the totality of the data, it should be considered as a likely benign variant. |