Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV002282719 | SCV002570111 | pathogenic | Rubinstein-Taybi syndrome due to CREBBP mutations | criteria provided, single submitter | clinical testing | ||
Gene |
RCV003443022 | SCV004167861 | pathogenic | not provided | 2023-04-08 | criteria provided, single submitter | clinical testing | Reported in two unrelated patients in the published literature with features consistent with a CREBBP-related disorder (Spena et al., 2014); Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 26485669, 29637745, 33063428, 25388907) |