Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001837202 | SCV002097691 | uncertain significance | Rubinstein-Taybi syndrome due to CREBBP mutations | 2020-06-18 | criteria provided, single submitter | clinical testing | The inherited p.Val293Glumissense variant identified in CREBBP has not been reported in affected individuals in the literature. The variantis absent from the gnomAD database indicating it is an extremely rare allele in the general population. The variant affects an evolutionarily conserved residueand is predicted deleterious by multiple in silico prediction tools. Based on the available evidence, the inherited p.Val293Glu missense variant identified inthis individual is assessed as a variant of uncertain significance. |