Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001362845 | SCV001558888 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2P; Muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A9 | 2020-10-23 | criteria provided, single submitter | clinical testing | This sequence change results in a premature translational stop signal in the DAG1 gene (p.Arg739Glyfs*3). While this is not anticipated to result in nonsense mediated decay, it is expected to disrupt the last 157 amino acid(s) of the DAG1 protein. This variant is not present in population databases (ExAC no frequency). This variant has not been reported in the literature in individuals with DAG1-related conditions. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Institute for Clinical Genetics, |
RCV003238361 | SCV002010673 | likely pathogenic | not provided | 2021-11-03 | criteria provided, single submitter | clinical testing |