Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Centre for Mendelian Genomics, |
RCV000415085 | SCV000492925 | pathogenic | Cardiac arrhythmia; Sudden cardiac death; Ventricular fibrillation; Aortic dilatation; Bicuspid aortic valve | 2014-06-10 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV003532098 | SCV004363337 | pathogenic | Cardiomyopathy | 2022-06-14 | criteria provided, single submitter | clinical testing | This variant changes 1 nucleotide in exon 18 of the DSP gene, creating a premature translation stop signal. This variant is expected to result in an absent or non-functional protein product. To our knowledge, this variant has not been reported in individuals affected with cardiovascular disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). Loss of DSP function is a known mechanism of disease (clinicalgenome.org). Based on the available evidence, this variant is classified as Pathogenic. |