Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001186754 | SCV001353332 | uncertain significance | Cardiomyopathy | 2020-06-30 | criteria provided, single submitter | clinical testing | This missense variant replaces glycine with serine at codon 168 of the DSP protein. Computational prediction suggests that this variant may not impact protein structure and function (internally defined REVEL score threshold <= 0.5, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with cardiovascular disorders in the literature. This variant has been identified in 1/251294 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Labcorp Genetics |
RCV002559946 | SCV003460460 | likely benign | Arrhythmogenic cardiomyopathy with wooly hair and keratoderma; Arrhythmogenic right ventricular dysplasia 8 | 2023-05-01 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV004807410 | SCV005428789 | uncertain significance | Arrhythmogenic cardiomyopathy with wooly hair and keratoderma | 2024-07-10 | criteria provided, single submitter | clinical testing | This missense variant replaces glycine with serine at codon 168 of the DSP protein. Computational prediction suggests that this variant may not impact protein structure and function (internally defined REVEL score threshold <= 0.5, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with DSP-related disorders in the literature. This variant has been identified in 1/251294 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV004994298 | SCV005575878 | uncertain significance | Cardiovascular phenotype | 2024-07-04 | criteria provided, single submitter | clinical testing | The p.G168S variant (also known as c.502G>A), located in coding exon 4 of the DSP gene, results from a G to A substitution at nucleotide position 502. The glycine at codon 168 is replaced by serine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |