Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Agnes Ginges Centre for Molecular Cardiology, |
RCV000853451 | SCV000996362 | uncertain significance | Primary dilated cardiomyopathy | 2017-04-06 | criteria provided, single submitter | research | The DSP Asp2436Glu variant has not been reported previously, and is absent from the 1000 genomes project (http://www.1000genomes.org/), as well as the large Exome Aggregation Consortium dataset (http://exac.broadinstitute.org/). Our lab has identified this variant in 1 DCM proband, as well as one affected sibling. Computational tools SIFT, PolyPhen2 and MutationTaster predict this variant to be deleterious. There is not enough evidence to fully support either a benign or pathogenic role, therefore we classify DSP Asp2436Glu as a variant of "uncertain significance". |