Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001053980 | SCV001218271 | pathogenic | Cataract 6 multiple types | 2019-12-30 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant results in an extension of the EPHA2 protein. Other variant(s) that result in a similarly extended protein product (p.Ile976Hisfs*37) have been determined to be pathogenic (PMID: 24940039). This suggests that these extensions are likely to be causative of disease. This variant has been reported to affect EPHA2 protein function (PMID: 22570727, 26900323). This variant has been observed in individual(s) with autosomal dominant congenital cataracts (PMID: 19306328, Invitae). This variant is also known as c.2915_2916delTG (p.V972GfsX39) in the literature. This variant is not present in population databases (ExAC no frequency). This sequence change results in a frameshift in the EPHA2 gene (p.Val972Glyfs*40). While this is not anticipated to result in nonsense mediated decay, it is expected to disrupt the last 5 amino acids of the EPHA2 protein and extend the protein by an additional 34 amino acids. |
OMIM | RCV001053980 | SCV000034418 | pathogenic | Cataract 6 multiple types | 2009-05-01 | no assertion criteria provided | literature only |