Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV003985222 | SCV004801581 | uncertain significance | Weaver syndrome | 2019-08-30 | criteria provided, single submitter | clinical testing | The EZH2 c.2111-3_2115dupCAGTTATG p.(Met706GlnfsTer3) variant causes a shift in the protein reading frame that is predicted to result in premature termination of the protein. Loss of normal protein function through either protein truncation or nonsense-mediated mRNA decay is expected. To our knowledge, this variant has not been reported in the peer-reviewed literature. This variant is not observed in version 2.1.1 or version 4.0.0 of the Genome Aggregation Database. Based on the available evidence the c.2111-3_2115dupCAGTTATG p.(Met706GlnfsTer3) variant is classified as a variant of uncertain significance for Weaver syndrome. |