Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Foundation for Research in Genetics and Endocrinology, |
RCV001789613 | SCV002029251 | uncertain significance | HSD10 mitochondrial disease | 2021-07-12 | criteria provided, single submitter | research | A hemizygous missense variation in exon 6 of the HSD17B10 gene that results in the amino acid substitution of Histidine for Glutamine at codon 220 was detected. The observed variant c.660A>C (p.Gln220His) has not been reported in the 1000 genomes and gnomAD databases. The in-silico prediction of the variant are damaging by LRT and MutationTaster2. The reference codon is conserved across species. Segregation analysis showed the variant to be of maternal origin. In summary, the variant meets our criteria to be classified as a variant of uncertain significance. |