Total submissions: 2
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Gene |
RCV004723269 | SCV005334650 | uncertain significance | not provided | 2023-08-27 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Variants in candidate genes are classified as variants of uncertain significance in accordance with ACMG guidelines (Richards et al., 2015) |
| Undiagnosed Diseases Network, |
RCV003329220 | SCV004035080 | uncertain significance | KIF5B-related osteogenesis imperfecta syndrome | 2021-08-25 | no assertion criteria provided | clinical testing |