Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001810351 | SCV002056062 | pathogenic | not provided | 2022-01-06 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Institute of Human Genetics, |
RCV004804254 | SCV005423809 | likely pathogenic | Complex cortical dysplasia with other brain malformations 2 | 2024-12-12 | criteria provided, single submitter | clinical testing | PS2_moderate, PM1, PM2, PP2, PP3 |