Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Medical Genetics, |
RCV004596025 | SCV005091010 | likely pathogenic | Microcephaly with or without chorioretinopathy, lymphedema, or intellectual disability | 2023-09-18 | criteria provided, single submitter | clinical testing | PVS1, PS2, PM2 - Low frequency in gnomAD population databases. In silico prediction tools estimated that the variant could be damaging for the protein function/stracture. Loss-of-function is a known mechanism of disease for this gene. The variant was detected de-novo (paternity confirmed). |