Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Johns Hopkins Genomics, |
RCV001290362 | SCV001478413 | likely pathogenic | Donnai-Barrow syndrome | 2021-01-29 | criteria provided, single submitter | clinical testing | This frameshift variant results in a premature stop codon, likely leading to nonsense-mediated decay and lack of protein production. LRP2 c.13568delA is absent from a large population dataset and has not been reported in ClinVar nor the literature, to our knowledge. We consider this variant to be likely pathogenic. |