Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
SIB Swiss Institute of Bioinformatics | RCV001267638 | SCV001593244 | uncertain significance | Neurodevelopmental disorder with microcephaly, impaired language, and gait abnormalities | 2021-05-10 | criteria provided, single submitter | curation | This variant is interpreted as a variant of uncertain significance for Neurodevelopmental disorder with microcephaly, impaired language, and gait abnormalities, autosomal recessive. The following ACMG Tag(s) were applied: Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium (PM2); Cosegregation with disease in multiple affected family members in a gene definitively known to cause the disease (PP1); Well-established functional studies show a deleterious effect (PS3 downgraded to supporting). |
OMIM | RCV001267638 | SCV001445822 | pathogenic | Neurodevelopmental disorder with microcephaly, impaired language, and gait abnormalities | 2020-11-18 | no assertion criteria provided | literature only |