Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004589500 | SCV005079204 | pathogenic | not provided | 2023-04-17 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation, as the last 488 amino acids are replaced with 2 different amino acids, and other loss-of-function variants have been reported downstream in HGMD; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 19533773) |
OMIM | RCV000007740 | SCV000027941 | pathogenic | Brachydactyly type B1 | 2009-07-01 | no assertion criteria provided | literature only |