Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Bondeson Group, |
RCV000735897 | SCV000747901 | pathogenic | Intellectual disability, X-linked, syndromic 33 | criteria provided, single submitter | research | The p.Arg1190Cys variant has been reported in two affected males of a large kindred of 5 generations. The variant is confirmed to segregate with the phenotype in 17 family members of three generations. Female carrier show skewed X-chromosome inactivation. | |
Genome Medicine, |
RCV000735897 | SCV000998771 | likely pathogenic | Intellectual disability, X-linked, syndromic 33 | 2019-09-23 | no assertion criteria provided | clinical testing |