Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001908861 | SCV002173654 | uncertain significance | BAP1-related tumor predisposition syndrome | 2021-08-28 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with BAP1-related conditions. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This sequence change replaces asparagine with serine at codon 515 of the BAP1 protein (p.Asn515Ser). The asparagine residue is moderately conserved and there is a small physicochemical difference between asparagine and serine. This variant is not present in population databases (ExAC no frequency). |
Center for Genomic Medicine, |
RCV003493890 | SCV004243163 | uncertain significance | not specified | 2025-03-04 | criteria provided, single submitter | clinical testing |