Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004720159 | SCV005324919 | likely pathogenic | not provided | 2023-09-07 | criteria provided, single submitter | clinical testing | Published functional studies found this variant results in abnormal splicing leading to reduced mRNA and protein expression (Nagata K et al., 2017); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 23808592, 29132416) |
Suma Genomics | RCV004759442 | SCV005367935 | uncertain significance | Distal arthrogryposis type 5D | criteria provided, single submitter | clinical testing | A missense variant c.1819G>A, p.(Gly607Ser) is observed in exon 13 of ECEL1 in trans with another variant. This variant is not observed in the gnomAD database. The in-silico analysis tool REVEL consistently predicts that this variant is disease-causing. ACMG criteria: PM2_Supporting and PP3 |