Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV000006232 | SCV003841426 | pathogenic | Wolcott-Rallison dysplasia | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. This variant was predicted to result in a loss or disruption of normal protein function through nonsense-mediated decay (NMD) or protein truncation. Multiple pathogenic variants are reported downstream of the variant. The variant has been reported to be associated with EIF2AK3 related disorder (ClinVar ID: VCV000005874 / PMID: 10932183). Therefore, this variant is classified as Pathogenic according to the recommendation of ACMG/AMP guideline. |
OMIM | RCV000006232 | SCV000026414 | pathogenic | Wolcott-Rallison dysplasia | 2000-08-01 | no assertion criteria provided | literature only |