Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000038257 | SCV000061926 | pathogenic | Noonan syndrome | 2009-11-04 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001209740 | SCV001381189 | uncertain significance | RASopathy | 2019-05-23 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C35"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has been reported as a recurrent variant in tumors (PMID: 26985062); however, this variant has not been reported as a germline variant in affected individuals. ClinVar contains an entry for this variant (Variation ID: 45115). This variant is not present in population databases (ExAC no frequency). This sequence change replaces glutamine with arginine at codon 61 of the KRAS protein (p.Gln61Arg). The glutamine residue is highly conserved and there is a small physicochemical difference between glutamine and arginine. |
Genome Diagnostics Laboratory, |
RCV001813342 | SCV002060771 | uncertain significance | Noonan syndrome and Noonan-related syndrome | 2021-02-03 | criteria provided, single submitter | clinical testing | |
Database of Curated Mutations |
RCV000420152 | SCV000504446 | pathogenic | Neoplasm of the large intestine | 2015-07-14 | no assertion criteria provided | literature only | |
Database of Curated Mutations |
RCV000431260 | SCV000504447 | pathogenic | Non-small cell lung carcinoma | 2014-10-02 | no assertion criteria provided | literature only | |
Database of Curated Mutations |
RCV000438012 | SCV000504448 | pathogenic | Thyroid tumor | 2014-10-02 | no assertion criteria provided | literature only | |
Key Laboratory of Carcinogenesis and Cancer Invasion, |
RCV003996395 | SCV004042811 | likely pathogenic | Lung cancer | no assertion criteria provided | clinical testing |