Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004549454 | SCV004105185 | likely pathogenic | KRAS-related disorder | 2022-10-12 | criteria provided, single submitter | clinical testing | The KRAS c.35G>C variant is predicted to result in the amino acid substitution p.Gly12Ala. To our knowledge, this variant has not been reported as a germline variant in individuals with Noonan/RASopathy phenotypes. However, several KRAS missense variants affecting Gly12, including p.Gly12Ala, have been reported as a somatic variant in multiple cancers (see for example - Brose et al. 2002. PubMed ID: 12460918; Lièvre et al. 2006. PubMed ID: 16618717). This variant has not been reported in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. This variant is interpreted as likely pathogenic. |
Juno Genomics, |
RCV004795958 | SCV005416700 | pathogenic | Familial cancer of breast; Noonan syndrome 3; Linear nevus sebaceous syndrome; Toriello-Lacassie-Droste syndrome; Cerebral arteriovenous malformation; Malignant tumor of urinary bladder; Autoimmune lymphoproliferative syndrome type 4; Acute myeloid leukemia; Cardiofaciocutaneous syndrome 2; Familial pancreatic carcinoma; Gastric cancer; Lung cancer | criteria provided, single submitter | clinical testing | PM2_Supporting+PM5_Strong+PP3_Moderate+PS4 | |
Laboratory for Molecular Medicine, |
RCV000038266 | SCV000061935 | pathogenic | Non-small cell lung carcinoma | 2007-12-07 | no assertion criteria provided | clinical testing | |
Xiao lab, |
RCV000984117 | SCV001132087 | pathogenic | Multiple myeloma | 2019-08-31 | no assertion criteria provided | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV001355876 | SCV001550889 | pathogenic | not provided | no assertion criteria provided | clinical testing | ||
Institute of Medical Sciences, |
RCV001374446 | SCV001571410 | pathogenic | Gallbladder cancer | 2020-10-30 | no assertion criteria provided | research | |
Key Laboratory of Carcinogenesis and Cancer Invasion, |
RCV003996396 | SCV004042812 | likely pathogenic | Lung cancer | no assertion criteria provided | clinical testing |