Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002211007 | SCV002496343 | likely pathogenic | not provided | 2021-10-04 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV002211007 | SCV002965672 | uncertain significance | not provided | 2021-12-30 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Arg67*) in the NDUFA9 gene. It is expected to result in an absent or disrupted protein product. However, the current clinical and genetic evidence is not sufficient to establish whether loss-of-function variants in NDUFA9 cause disease. This variant is present in population databases (rs758574474, gnomAD 0.006%). This variant has not been reported in the literature in individuals affected with NDUFA9-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |