Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003089786 | SCV003476212 | uncertain significance | not provided | 2024-10-24 | criteria provided, single submitter | clinical testing | This sequence change replaces histidine, which is basic and polar, with tyrosine, which is neutral and polar, at codon 444 of the NDUFS1 protein (p.His444Tyr). This variant is present in population databases (rs373339826, gnomAD 0.01%). This variant has not been reported in the literature in individuals affected with NDUFS1-related conditions. ClinVar contains an entry for this variant (Variation ID: 2161999). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is not expected to disrupt NDUFS1 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV003078856 | SCV003701200 | uncertain significance | Inborn genetic diseases | 2021-10-06 | criteria provided, single submitter | clinical testing | The c.1330C>T (p.H444Y) alteration is located in exon 13 (coding exon 12) of the NDUFS1 gene. This alteration results from a C to T substitution at nucleotide position 1330, causing the histidine (H) at amino acid position 444 to be replaced by a tyrosine (Y). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003134642 | SCV003813530 | uncertain significance | Mitochondrial complex 1 deficiency, nuclear type 5 | 2019-05-21 | criteria provided, single submitter | clinical testing |