Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003487095 | SCV004236078 | uncertain significance | Megalencephaly-polymicrogyria-polydactyly-hydrocephalus syndrome 1 | 2023-06-22 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003487095 | SCV004270269 | uncertain significance | Megalencephaly-polymicrogyria-polydactyly-hydrocephalus syndrome 1 | 2023-07-12 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gly87Serfs*14) in the PIK3R2 gene. It is expected to result in an absent or disrupted protein product. However, the current clinical and genetic evidence is not sufficient to establish whether loss-of-function variants in PIK3R2 cause disease. This variant is present in population databases (rs778790424, gnomAD 0.01%). This variant has not been reported in the literature in individuals affected with PIK3R2-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |