Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000622868 | SCV000742659 | uncertain significance | Inborn genetic diseases | 2017-06-19 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001301597 | SCV001490772 | likely benign | Norman-Roberts syndrome; Familial temporal lobe epilepsy 7 | 2024-04-17 | criteria provided, single submitter | clinical testing | |
Center for Genomics, |
RCV001301597 | SCV002495922 | uncertain significance | Norman-Roberts syndrome; Familial temporal lobe epilepsy 7 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature but is present in 0.02% (2/67960) of European alleles in the Genome Aggregation Database (https://gnomad.broadinstitute.org/variant/7 103561864 C T?dataset=gnomad_r3). This variant is present in ClinVar (Variation ID:521876). Evolutionary conservation and computational predictive tools suggest that this variant may impact the protein. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. | |
Gene |
RCV004767448 | SCV005376408 | uncertain significance | not provided | 2023-11-03 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |