Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Fulgent Genetics, |
RCV002493480 | SCV002784345 | uncertain significance | Congenital myasthenic syndrome 11; Fetal akinesia deformation sequence 2 | 2022-05-16 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004035473 | SCV004936879 | uncertain significance | Inborn genetic diseases | 2024-02-17 | criteria provided, single submitter | clinical testing | The c.985C>T (p.H329Y) alteration is located in exon 7 (coding exon 7) of the RAPSN gene. This alteration results from a C to T substitution at nucleotide position 985, causing the histidine (H) at amino acid position 329 to be replaced by a tyrosine (Y). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Natera, |
RCV001278482 | SCV001465496 | uncertain significance | Congenital myasthenic syndrome | 2020-04-13 | no assertion criteria provided | clinical testing |